The full form of BASM in medical term is “Biliary Atresia Splenic Malformation.”
Biliary atresia splenic malformation, or BASM, is a rare congenital condition affecting the liver and spleen. It is characterized by the absence or malformation of the bile ducts that carry bile from the liver to the gallbladder, accumulating bile and liver damage.
Biliary atresia is a condition that occurs in infants. Symptoms of BASM typically develop within the first few weeks of life and may include jaundice, dark urine, pale stools, and an enlarged liver and spleen. BASM can lead to cirrhosis, liver failure, and death if left untreated.
The diagnosis of BASM is typically made through a combination of physical examination, blood tests, imaging studies, and liver biopsy. Treatment of the condition involves surgery to restore bile flow and prevent further damage to the liver. In some cases, liver transplantation may be necessary.
Several surgical procedures can be used to treat BASM, including the Kasai procedure, which involves removing the damaged bile ducts and replacing them with a segment of the intestine. This procedure is most successful.
In addition to surgery, infants with BASM may require medications and nutritional support to manage their symptoms and prevent complications. Regular monitoring and follow-up care are also important to ensure optimal outcomes. While BASM is a rare and serious condition, early diagnosis and treatment can greatly improve the long-term outlook for affected infants and thereby offer possible care for these patients.